Bilateral ovarian cystic lymphangioma with chylous ascitis in pregnancy - a rare case report with review


  • Archana Daddenavar Daddenavar Hospital, Bagalkot, Karnataka, India
  • Vikas Daddenavar Daddenavar Hospital, Bagalkot, Karnataka, India
  • Rashmi Patil St Martha’s Hospital, Bangalore, Karnataka, India



Lymphangioma, Ovary, Chylous ascites, Pregnancy


Bilateral lymphangioma of the ovary being an extremely rare lesion, with chylous ascites and full term pregnancy, this is the first ever case in the world to be reported. Chylous ascites with pregnancy only 5 cases have been reported earlier. And above all, only 20 cases of ovarian lymphangioma are reported in the literature so far. Lymphangioma is usually asymptomatic and unilateral, presenting as an incidental finding during routine gynaecologic procedures. It is made up of aggregates of lymphatic spaces in ovarian stroma and the endothelial cells lining these spaces. The main differential diagnosis is an adenomatoid tumour which can be differentiated from the lymphangioma by immunohistochemical studies. We report this rare lesion in a case of 28 years old primigravida with 37 weeks of gestation with pregnancy induced hypertension with acute distension of abdomen with respiratory distress.


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