A rare case of aggressive angiomyxoma of vulva since childhood

Authors

  • Shankar B. Burute Department of Obstetrics & Gynaecology, DY Patil Medical College, Pune, Maharashtra, India
  • T. Swetha Jahnavi Department of Obstetrics & Gynaecology, DY Patil Medical College, Pune, Maharashtra, India
  • Karuna Ratwani Department of Obstetrics & Gynaecology, DY Patil Medical College, Pune, Maharashtra, India
  • Arpana A. Dharwadkar Department of Pathology, DY Patil Medical College, Pune, Maharashtra, India
  • Jayashree P. Kulkarni Department of Obstetrics & Gynaecology, DY Patil Medical College, Pune, Maharashtra, India

Keywords:

Aggressive angiomyxoma, Mesenchymal tumors, Vulval mass

Abstract

Aggressive angiomyxoma is a locally invasive benign mesenchymal tumour usually occurring in women of reproductive age and is rare in children. It carries a high risk of recurrence and hence needs to be differentiated from other masses. The diagnosis is difficult clinically and is almost always histological. Here is a rare case of aggressive angiomyxoma of vulva in a 15 year old female presented with presented with mass in vulva on left side since birth and increased to the present size since 3 years. The swelling was painless, no local rise of temperature, no visible veins. Attained menarche 2 years ago and cycles are regular with normal flow.

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Published

2017-01-04