DOI: https://dx.doi.org/10.18203/2320-1770.ijrcog20221689
Published: 2022-06-27

Aggressive angiomyxoma of uterine corpus

Rachitha Revanna, Padmasri Ramalingappa, Divya Tumkur Kumar

Abstract


Aggressive angiomyxoma (AA) is a rare slow growing mesenchymal tumour that preferentially involves the vulvovaginal, pelvic or perineal regions. It is called aggressive due its frequent local recurrences and infiltrative behavior. They occur most commonly in the reproductive age group in women. A 37 year old with AA of endometrial polyp, presenting with acute pain abdomen and friable, fleshy mass protruding out of introitus, precipitated by a dilatation and curettage for heavy menstrual bleeding. A clinical diagnosis of fibroid polyp with acute red degeneration was considered. There was a spontaneous expulsion of fleshy mass. HPE showed AA with features of torsion. MRI showed T2 heterogenous hyperintense mass lesion of 9 x 3 x 3.9 cm pedunculated polypoidal arising from upper anterior uterine wall. Hysterectomy specimen confirmed HPE findings of AA. Radiological studies and pathological evaluation aids in the diagnosis and planning of appropriate treatment of AA. Close and long term follow up of these patients should be emphasized due to high rate of local recurrence.


Keywords


Aggressive angiomyxoma, Mesenchymal tumor, Myxoid matrix

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References


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