A case of partial empty sella turcica syndrome: Sheehan syndrome
DOI:
https://doi.org/10.18203/2320-1770.ijrcog20222332Keywords:
Partial empty sella turcica syndrome, Sheehan syndrome, Necrosis of pituitary glandAbstract
Sheehan syndrome is the clinical manifestation that results due to necrosis of pituitary gland resulting from severe postpartum haemorrhage during pregnancy and is one of the causes of empty sella, complete absence of the pituitary gland. Partial empty sella is the term given when part of the gland is visible on imaging. The hormonal deficiencies and resulting clinical syndromes are thus respectively named as complete/empty sella syndrome and partial empty sella syndrome. Incidence of empty sella especially partial empty sella are extremely rare. Also, Sheehan syndrome as a cause of the same has not been frequently observed. Here, we present a case of a young female who presented with secondary amenorrhoea postpartum and was diagnosed ultimately to have partial empty sella syndrome and partial Sheehan syndrome.
References
NORD. Information on Clinical Trials and Research Studies. Available at: https://rarediseases.org/for-patients-and-families/yuval/information resources/news-patient-recruitment. Accessed on 24 March 2022.
Kelestimur F. Sheehan’s syndrome. Pituitary. 2003;6:181-8.
Karaca Z, Laway BA, Dokmetas HS, Atmaca H, Kelestimur F. Sheehan syndrome. Nat Rev Dis Primers. 2016;2:16092.
Kristjansdottir HL, Bodvarsdottir SP, Sigurjonsdottir HA. Sheehan's syndrome in modern times: a nationwide retrospective study in Iceland. Eur J Endocrinol. 2011;164(3):349-54.
Zargar AH, Singh B, Laway BA, Masoodi SR, Wani AI, Bashir MI. epidemiologic aspects of postpartum pituitary hypofunction (sheehan syndrome) fertile. Fertil Steril. 2005;84(2):523-8.
Karaca Z, Hacioglu A, Kelestimur F. neuroendocrine changes after aneurysmal subarachnoid haemorrhage. Pituitary. 2019;22(3):305-21.
Thompson CJ, Costello RW, Crowley RK. Management of hypothalamic disease in patients with craniopharyngioma. Clin endocrinol (oxf.) 2019;90(4):506-16.
Dash RJ, Gupta V, Suri S. Sheehan syndrome clinical profile. Aust N Zeal J Med. 1993;23:26-31.
Haddock L, Vega LA, Augito F, Rodriguez O. Adrenocortical thyroidal and human growth hormone reserve in sheehan syndrome. John Hopkins Med J. 1972;131:80-99.
Shahmanesh M. Pituitary function tests in sheehan syndrome. Clin Endocrinol. 1980;12:303-11.
Matsuzaki S, Endo M, Ueda Y, Mimura K, Kakigano A, Egawa-Takata T, et al. A case of acute Sheehan's syndrome and literature review: a rare but life-threatening complication of postpartum hemorrhage. BMC Pregnancy Childbirth. 2017;17(1):188.