A case of partial empty sella turcica syndrome: Sheehan syndrome

Authors

  • Lata Assudani Department of Obstretrics and Gynecology, GGMC and JJ Group of Hospitals, Mumbai, Maharashtra, India
  • Ashish Notwani Department of Neonatology, Seth G.S. and KEM hospital, Mumbai, Maharashtra, India

DOI:

https://doi.org/10.18203/2320-1770.ijrcog20222332

Keywords:

Partial empty sella turcica syndrome, Sheehan syndrome, Necrosis of pituitary gland

Abstract

Sheehan syndrome is the clinical manifestation that results due to necrosis of pituitary gland resulting from severe postpartum haemorrhage during pregnancy and is one of the causes of empty sella, complete absence of the pituitary gland. Partial empty sella is the term given when part of the gland is visible on imaging. The hormonal deficiencies and resulting clinical syndromes are thus respectively named as complete/empty sella syndrome and partial empty sella syndrome. Incidence of empty sella especially partial empty sella are extremely rare. Also, Sheehan syndrome as a cause of the same has not been frequently observed. Here, we present a case of a young female who presented with secondary amenorrhoea postpartum and was diagnosed ultimately to have partial empty sella syndrome and partial Sheehan syndrome.

Author Biographies

Lata Assudani, Department of Obstretrics and Gynecology, GGMC and JJ Group of Hospitals, Mumbai, Maharashtra, India

Senior Resident department of obstretrics and gynecology

Ashish Notwani, Department of Neonatology, Seth G.S. and KEM hospital, Mumbai, Maharashtra, India

Seth G.S government medical college and KEM hospitalacase

References

NORD. Information on Clinical Trials and Research Studies. Available at: https://rarediseases.org/for-patients-and-families/yuval/information resources/news-patient-recruitment. Accessed on 24 March 2022.

Kelestimur F. Sheehan’s syndrome. Pituitary. 2003;6:181-8.

Karaca Z, Laway BA, Dokmetas HS, Atmaca H, Kelestimur F. Sheehan syndrome. Nat Rev Dis Primers. 2016;2:16092.

Kristjansdottir HL, Bodvarsdottir SP, Sigurjonsdottir HA. Sheehan's syndrome in modern times: a nationwide retrospective study in Iceland. Eur J Endocrinol. 2011;164(3):349-54.

Zargar AH, Singh B, Laway BA, Masoodi SR, Wani AI, Bashir MI. epidemiologic aspects of postpartum pituitary hypofunction (sheehan syndrome) fertile. Fertil Steril. 2005;84(2):523-8.

Karaca Z, Hacioglu A, Kelestimur F. neuroendocrine changes after aneurysmal subarachnoid haemorrhage. Pituitary. 2019;22(3):305-21.

Thompson CJ, Costello RW, Crowley RK. Management of hypothalamic disease in patients with craniopharyngioma. Clin endocrinol (oxf.) 2019;90(4):506-16.

Dash RJ, Gupta V, Suri S. Sheehan syndrome clinical profile. Aust N Zeal J Med. 1993;23:26-31.

Haddock L, Vega LA, Augito F, Rodriguez O. Adrenocortical thyroidal and human growth hormone reserve in sheehan syndrome. John Hopkins Med J. 1972;131:80-99.

Shahmanesh M. Pituitary function tests in sheehan syndrome. Clin Endocrinol. 1980;12:303-11.

Matsuzaki S, Endo M, Ueda Y, Mimura K, Kakigano A, Egawa-Takata T, et al. A case of acute Sheehan's syndrome and literature review: a rare but life-threatening complication of postpartum hemorrhage. BMC Pregnancy Childbirth. 2017;17(1):188.

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Published

2022-08-29

Issue

Section

Case Reports