Presence of fibroids in the absence of uterus- Mayer-Rokitansky-Küster-Hauser syndrome with fibroids: a case report
DOI:
https://doi.org/10.18203/2320-1770.ijrcog20231589Keywords:
MRKH syndrome, Fibroids, Laparoscopic myomectomy, Davydov’s vaginoplastyAbstract
Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome is rare congenital anomaly with complete absence of uterus and upper part of vagina. Fibroids are one of the most common benign tumours arising in women. Fibroids arising from Mullerian remnants are very rare. These fibroids often pose difficulty in diagnosis and management. Here, we report a rare case of fibroids arising from Mullerian remnants in MRKH syndrome and the treatment provided for the patient.
References
Morcel K, Camborieux L, Guerrier D. Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome. Orphanet J Rare Dis. 2007;2(1):13.
Farris M, Bastianelli C, Rosato E, Brosens I, Benagiano G. Uterine fibroids: an update on current and emerging medical treatment options. Ther Clin Risk Manag. 2019;15:157.
Raziel A, Friedler S, Gidoni Y, Ben Ami I, Strassburger D, Ron-El R. Surrogate in vitro fertilization outcome in typical and atypical forms of Mayer–Rokitansky–Küster–Hauser syndrome. Human Reproduction. 2012;27(1):126-30.
Georgopapadakos N, Manoli A, Passia G, Skandalakis PN, Filippou D. Uterus Transplantation as a Therapy Method in Mayer-Rokitansky-Küster-Hauser Syndrome. Cureus. 2019;11(12).
Baker J, Buttini M. Fibroid arising in a müllerian duct remnant and presenting as a pelvic mass in a patient with vaginal agenesis: an unusual finding. Aust N Z J Obstet Gynaecol. 1995;35(3):340-1.
Amaratunga T, Kirkpatrick I, Yan Y, Karlicki F. Ectopic Pelvic Fibroid in a Woman With Uterine Agenesis and Mayer-Rokitansky-Küster-Hauser Syndrome. Ultrasound Q. 2017;33(3):237-41.
Jain N, Kriplani I, Sharma S, Hanumantaiya S, Kriplani A. Urinary retention unveiling deeply embedded multiple leiomyomas in women with Mayer–Rokitansky–Kuster–Hauser syndrome and its successful laparoscopic management: a case-report and literature review. J Surg Case Rep. 2022;2022(6).
