A rare presentation of non-cirrhotic portal fibrosis in pregnancy: a case report
DOI:
https://doi.org/10.18203/2320-1770.ijrcog20250206Keywords:
Non cirrhotic portal fibrosis, Pregnancy, Portal hypertensionAbstract
Non cirrhotic portal fibrosis (NCPF) in pregnancy is a rare occurrence with an in hospital incidence of 0.009%. Management in pregnancy is challenging due to lack of standard protocol and paucity of extensive research in current literature. NCPF if untreated can lead to catastrophic complications and lead to significant maternal morbidity and mortality. We present a case report of a 23-year-old G2A1 female presenting for the first time in pregnancy at 34 weeks’ gestation as a case of NCPF with prelabour rupture of membranes. She was managed with multidisciplinary approach and underwent normal vaginal delivery with satisfactory feto-maternal outcome. NCPF in pregnancy is uncommon and a thorough knowledge about the condition and systematic management at a tertiary care center with a multidisciplinary team is essential. Its prognosis in pregnancy is usually good if managed promptly and systematically.
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Sarin SK, Kumar A, Chawla YK, Baijal SS, Dhiman RK, Jafri W, et al. Noncirrhotic portal fibrosis/idiopathic portal hypertension: APASL recommendations for diagnosis and treatment. Hepatol Int. 2007;1(3):398-413. DOI: https://doi.org/10.1007/s12072-007-9010-9
Kochhar R, Kumar S, Goel RC, Sriram PV, Goenka MK, Singh K. Pregnancy and its outcome in patients with noncirrhotic portal hypertension. Dig Dis Sci. 1999;44(7):1356-61. DOI: https://doi.org/10.1023/A:1026687315590
Andrade F, Shukla A, Bureau C, Senzolo M, D’Alteroche L, Heurgué A, et al. Pregnancy in idiopathic non-cirrhotic portal hypertension: A multicentric study on maternal and fetal management and outcome. J Hepatol. 2018;69(6):1242-9. DOI: https://doi.org/10.1016/j.jhep.2018.08.007
Aggarwal N, Sawhney H, Vasishta K, Dhiman RK, Chawla Y. Non-cirrhotic portal hypertension in pregnancy. Int J Gynaecol Obstet. 2001;72(1):1-7. DOI: https://doi.org/10.1016/S0020-7292(00)00263-0
Keepanasseril A, Gupta A, Ramesh D, Kothandaraman K, Jeganathan YS, Maurya DK. Maternal-fetal outcome in pregnancies complicated with non-cirrhotic portal hypertension: experience from a Tertiary Centre in South India. Hepatol Int. 2020;14(5):842-9. DOI: https://doi.org/10.1007/s12072-020-10067-5
Pol MM, Chawla LU, Rathore YS, Goel R. Combined caesarean with splenectomy in pregnancy with portal hypertension: defining plausibility. BMJ Case Rep. 2017;2017:bcr2017220561. DOI: https://doi.org/10.1136/bcr-2017-220561
Niroopama P. Pregnancy Complicated by Portal Hypertension Secondary to Noncirrhotic Portal Fibrosis. J South Asian Federation Obstet Gynaecol. 2017;9(1):63-5. DOI: https://doi.org/10.5005/jp-journals-10006-1460
Aggarwal N, Negi N, Aggarwal A, Bodh V, Dhiman RK. Pregnancy with portal hypertension. J Clin Exp Hepatol. 2014;4(2):163-71. DOI: https://doi.org/10.1016/j.jceh.2014.05.014
Schouten JNL, Garcia-Pagan JC, Valla DC, Janssen HLA. Idiopathic noncirrhotic portal hypertension. Hepatology. 2011;54(3):1071-81. DOI: https://doi.org/10.1002/hep.24422
Tan J, Surti B, Saab S. Pregnancy and cirrhosis. Liver Transplantation. 2008;14(8):1081-91. DOI: https://doi.org/10.1002/lt.21572
Safioleas MC, Moulakakis KG. A rare cause of intra-abdominal haemorrhage: spontaneous rupture of the splenic vein. Acta Chir Belg. 2006;106(2):237-9. DOI: https://doi.org/10.1080/00015458.2006.11679881
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