A rare case of aggressive angiomyxoma of vulva

Authors

  • Vilas Namdevrao Kurude Department of Obstetrics and Gynaecology, JJ Hospital, Grant Government Medical College, Mumbai, Maharashtra, India
  • Surbhi Sinha Department of Obstetrics and Gynaecology, JJ Hospital, Grant Government Medical College, Mumbai, Maharashtra, India

DOI:

https://doi.org/10.18203/2320-1770.ijrcog20162678

Keywords:

Aggressive angiomyxoma, Mesenchymal tumor, Vulval tumor

Abstract

Aggressive angiomyxoma is a rare, slow-growing soft tissue tumor developing from myxoid cells that usually arises in the pelvis and perineal regions of women in reproductive age, with a marked tendency to local recurrence but a low tendency to metastasize. It is often initially misdiagnosed because of its rarity. It has a marked tendency for local recurrence. Surgical resection is the treatment modality of choice for aggressive angiomyxoma. We describe a case of an aggressive angiomyxoma of vulva in a 75 year old postmenopausal woman with an asymptomatic mass on the genitalia since 3 years. Excision of the mass was done under local anaesthesia and the diagnosis was only made after histological examination. . The patient has been kept under follow-up. The etiology, presentation, diagnosis and management of this rare tumor are outlined. Angiomyxoma of vulva and vagina refers to a rare disease. Pre-operative diagnosis is difficult due to rarity and absence of diagnostic features, but it should be considered in every mass in genital, perianal and pelvic region in a woman in the reproductive age.

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References

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Published

2017-01-11

How to Cite

Kurude, V. N., & Sinha, S. (2017). A rare case of aggressive angiomyxoma of vulva. International Journal of Reproduction, Contraception, Obstetrics and Gynecology, 5(8), 2844–2846. https://doi.org/10.18203/2320-1770.ijrcog20162678

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Section

Case Reports