An interesting case report on obstructed labour with prune belly syndrome
DOI:
https://doi.org/10.18203/2320-1770.ijrcog20242513Keywords:
Prune belly syndrome, Abdominal distention, Bladder outlet obstruction, AnhydramniosAbstract
Prune belly syndrome is a rare disorder of uncertain etiology characterized by a triad of deficient abdominal musculature, cryptorchidism and urinary tract abnormalities. This condition varies in its severity which makes diagnosis challenging during early antenatal ultrasound scan. 34-year-old G4P3L3 who was counselled for pregnancy termination at 20 weeks in view of multiple anomalies detected on antenatal ultrasound. At 34 weeks of gestation presented to our institution in active phase of labour and progressed to obstructed labour and was managed by ultrasound guided fetal abdominal tapping. We conclude that suspicion of such anomalies through an early antenatal scan require further follow-up with an experienced ultrasonographer and maternal–fetal medicine specialist for a decision to be made antenatally regarding the course of pregnancy and delivery management based on the severity of the condition in a tertiary center.
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References
Routh JC, Huang L, Retik AB, Nelson CP. Contemporary epidemiology and characterization of newborn males with prune belly syndrome. Urology. 2010;76(1):44-8.
Zugor V, Schott GE, Labanaris AP. The prune belly syndrome: urological aspects and long-term outcomes of a rare disease. Pediatr Rep. 2012;4(2):20.
Seidel NE, Arlen AM, Smith EA, Kirsch AJ. Clinical manifestations and management of prune-belly syndrome in a large contemporary pediatric population. Urology. 2015;85(1):211-5.
Nunn IN, Stephens FD. The triad syndrome: a composite anomaly of the abdominal wall, urinary system and testes. J Urol.1961;86:782.
Wheatley JM, Stephens FD, Hutson JM. Prune-belly syndrome: ongoing controversies regarding pathogenesis and management. Semin Pediatr Surg. 1996;5(2):95-106.
Hassett S, Smith GH, Holland AJ. Prune belly syndrome. Pediatr Surg Int. 2012;28(3):219-28.
Tagore KR, Ramineni AK, Vijaya Lakshmi AR, Bhavani N. Prune Belly syndrome. Case Rep Pediatr. 2011:1-3.
Prune belly syndrome-symptoms, causes, treatment. 2007. National Organization for Rare Disorders (NORD). Available at https://rarediseases.org/rare-diseases/prune-belly. Accessed on 17th March 2023.
Ellison L, Cendron M, Ornvold K. Early diagnosis of fetal bladder outlet obstruction. J Pediatr Surg. 2000;35:513.
Leeners B, Sauer I, Schefels J, Cotarelo CL, Funk A. Prune-belly syndrome: therapeutic options including in utero placement of a vesicoamniotic shunt. J Clin Ultrasound. 2000;28(9):500-7.
Swaroop N, Sharma P, Kumari K, Seth S. Obstructed labour caused by rare congenital anomaly of foetus: managed by foetal abdominal tapping leading to successful vaginal delivery. Int J Reprod Contracept Obstet Gynecol. 2015;1220-2.
Cardoso PM, Surve S, Pednecar G, Mello AD. A rare fetal anomaly causing obstructed labour. J Evol Med Dent Sci. 2014;3(56):12829-33.