Clinicopathological characteristics and oncological outcomes in a case of primary ovarian adenosarcoma with sarcomatous differentiation: a case report and literature review

Sheereen Fatima; Imran N. Shaikh; Naseem I. Shaikh

doi:10.18203/2320-1770.ijrcog20253123

Authors

Sheereen Fatima Department of Radiation Oncology, Sir Hurkisondas Nurrotumdas Reliance Foundation Hospital and Research Centre, Mumbai, Maharashtra, India https://orcid.org/0009-0004-1796-2086
Imran N. Shaikh Centre for Cancer, Kokilaben Dhirubhai Ambani Hospital and Medical Research Institute, Four Bungalows, Mumbai, Maharashtra, India
Naseem I. Shaikh Department of Radiation Oncology, Sir Hurkisondas Nurrotumdas Reliance Foundation Hospital and Research Centre, Mumbai, Maharashtra, India

DOI:

https://doi.org/10.18203/2320-1770.ijrcog20253123

Keywords:

Adenosarcoma ovary, Mixed mullerian tumors, Ovarian tumors

Abstract

Mullerian adenosarcoma is a rare malignant tumor generally involving the uterine corpus but can uncommonly involve extrauterine organs. Ovarian adenosarcoma is extremely rare and often diagnosed in young women. Majority of them are low grade with a good prognosis except for adenosarcoma with sarcomatous overgrowth (SO). We report a case of a large sized ovarian adenosarcoma with SO with elevated levels Ca125 and Ca19.9 and having disease free interval of approximately 1.5 years.

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