Aggressive angiomyxoma of the vulva presenting as a massive perineal mass

Ramona Perhar; Snigdha Verma; Shikha Chaudhary

doi:10.18203/2320-1770.ijrcog20261645

Authors

Ramona Perhar Department of Obstetrics and Gynecology, M. L. N. Medical College, Prayagraj, Uttar Pradesh, India
Snigdha Verma Department of Obstetrics and Gynecology, M. L. N. Medical College, Prayagraj, Uttar Pradesh, India
Shikha Chaudhary Department of Obstetrics and Gynecology, M. L. N. Medical College, Prayagraj, Uttar Pradesh, India

DOI:

https://doi.org/10.18203/2320-1770.ijrcog20261645

Keywords:

Case report, Myxoid tumour, Surgical excision, MRI pelvis, Rare vulval tumour, Aggressive angiomyxoma, Vulval mass, Perineal tumour

Abstract

Aggressive angiomyxoma is a rare benign but locally infiltrative mesenchymal tumour that predominantly affects women of reproductive age. It commonly arises in the pelvis and perineal regions and is characterized by slow growth and a high recurrence rate. We report a case of a 39-year-old multiparous woman presenting with a progressively enlarging vulval swelling over 12 years. Imaging revealed a well-defined soft tissue lesion without infiltration of adjacent structures. Complete surgical excision was performed, and histopathological examination confirmed aggressive angiomyxoma. This case highlights the importance of considering aggressive angiomyxoma in the differential diagnosis of large vulval masses and emphasizes the role of complete surgical excision and long-term follow-up.

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