Herlyn-Werner-Wunderlich syndrome complicated with pyocolpos: an unusual cause of postabortal sepsis

Abstract

Obstructive mullerian anomalies give rise to a spectrum of clinical presentations and are uncommon in routine gynecologic practice. The patient usually becomes symptomatic in early reproductive years. Recurrent pelvic pain, dysmenorrhoea, enlarging abdominopelvic mass and abnormal vaginal discharge are the common presenting symptoms. We describe a rare case of a mullerian anomaly getting diagnosed 13 years after attaining menarche during evaluation of postabortal sepsis. Patient presented two weeks following evacuation done for missed abortion, with acute abdominal pain, fever and foul smelling discharge per vaginum. The anomaly was identified as uterus didelphys with obstructed left hemivagina and ipsilateral renal agenesis (Herlyn-Werner-Wunderlich syndrome) complicated by pyocolpos. She was successfully managed by single stage transvaginal septum resection under laparoscopic control.