A rare case of pregnancy with Sturge-Weber syndrome
DOI:
https://doi.org/10.18203/2320-1770.ijrcog20150112Keywords:
Sturge-Weber syndrome, Angioma, Glaucoma, Leptomeningeal angioma, Calcifications, Facial haemangiomaAbstract
Sturge-Weber syndrome is a rare sporadic neurocutaneous syndrome characterized by facial angiomas, ocular abnormalities (glaucoma and choroidal hemangioma), and leptomeningeal angioma. We report a case of Sturge Weber syndrome type I, associated with seizures, with gestational diabetes. She had successful labour outcome. Very few such cases have been reported in literature. The effect of pregnancy on neurological symptoms of Sturge Weber syndrome is not known.
References
Baselga E. Sturge-Weber syndrome. Semin Cutan Med Surg. 2004;23(2):87-98.
Roach ES. Neurocutaneous syndromes. Paediatr Clin North Am (Medline). 1992;39(4)591-620.
Takeoka M. Paediatric Sturge Weber Syndrome - clinical presentation, Medscape, 2010. Available at: http://emedicine.medscape.com/article/1177523-clinical. Accessed 20 May 2013.
Hennedique AA, Quabe AA, Al-Nakib K. Sturge Weber Syndrome & dermatological facial portwine stains; incidence, association with glaucoma and pulse tunable dye laser treatment effectiveness. Plast Reconstruc Surg. 2008;12(4):1173-80.
Gupta, Saini. Pregnancy with Sturge Weber syndrome presenting as status epilepticus. Indian J Med Case Rep. 2013 Apr-Jun;2(2):19-22.
Aziz AS, Hui D, Chinnappa V, Aviv RI, Swartz RH. Successful pregnancy, epidural anaesthesia, labour and delivery in a woman of Sturge Weber syndrome with previous hemespherectomy. J Obstet Gynaecol Can. 2013;35(10):917-9.
Tadrous R, Ni Mhuirchteagh R, McCaul C. Anaesthesia for caesarean section in a patient with Sturge-Weber syndrome following acute neurological deterioration. Int J Obstet Anesth. 2011;20(3):259-62.