Published: 2017-05-25

A challenging case of SLE associated with intrahepatic cholestasis and atypical Wilson's disease

Jyoti Kankanala


We herewith present a case of SLE which reflects that appropriate Multidisciplinary approach gives good outcome inspite of risk factors including prematurity. Systemic lupus erythematosus (SLE) an autoimmune disease in itself a high-risk factor along with intrahepatic cholestasis and atypical wilson's disease it’s a tough journey for clinicians as well as the family but good timely intervention by appriopriate investigations gave an excellent outcome. Emergency LSCS was performed for pathological CTG at 31 weeks, mother and child followed up for a year and a half then we are reporting this case.


Autoimmune diseases, Cholestasis, SLE, Wilson's disease

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