DOI: http://dx.doi.org/10.18203/2320-1770.ijrcog20163898

An unusual presentation of a rare tumour: aggressive angiomyxoma

Samar Rudra, Kanika Bajaj

Abstract


Aggressive angiomyxoma is a very rare variety of soft tissue tumour exclusively involves the vulvovagina, perineum and pelvic region of women of reproductive age group. We report the case of a 48-year old woman presented with gluteal mass. Nature of the mass could not be diagnosed by clinical radiological and imaging evaluation, however it was found to extend from pelvis to gluteal region. It was removed surgically. Histopathology revealed the mass to be aggressive angiomyxoma, a rare variety of pelviperineal tumour extended from pelvis to the gluteal region. AAM presenting as a gluteal mass is extremely rare.

Keywords


Aggressive angiomyxomas, Pelvic soft tissue tumour

Full Text:

PDF

References


Haldar K, Martinek IE. Aggressive angiomyxoma: A case series and literature review. EJSO - European Journal of Surgical Oncology, WB Saunders. 2010;36(4):335.

Steeper TA, Rosai J. Aggressive angiomyxoma of the pelvis and perineum: Report of nine cases of a distinctive type of gynaecologic soft tissue neoplasm. Am J Surg Pathol. 1983;7:463-75.

Micci F, Brandal P. Soft Tissue Tumors: Aggressive angiomyxoma. Atlas Genet Cytogenet Oncol Haematol. 2007.

Fetsch JF, Laskin WB, Lefkowitz M. Aggressive angiomyxoma: a clinicopathologic study of 29 female patients. Cancer. 1996;78:79-90.

Chen L, Schink JC, Panares BN. Resection of a giant aggressive angiomyxoma in the Philippines. Gynecol Oncol. 1998;70:435-9.

Siassi RM, Papadopoulos T, Matzel KE. Metastasizing aggressive angiomyxoma. N Engl J Med. 1999;341:1772.

Blandamura S, Cruz J, Faure-Vergara L. Aggressive angiomyxoma: a second case of metastasis with patient’s death. Hum Pathol. 2003;34:1072-4.

Smith OH, Worrell RV, Smith AY. Aggressive angiomyxoma of the female pelvis and perineum: review of the literature. Gynecol Oncol. 1991;42:79-85.

McCluggage WG, Jamieson T, Dobbs SP. Aggressive angiomyxoma of the vulva:dramatic response to gonadotropin-releasing hormone agonist therapy. Gynecol Oncol. 2006;100:623-5.