DOI: http://dx.doi.org/10.18203/2320-1770.ijrcog20175303

Aggressive angiomyxoma of vagina: a rare entity

Ruby Bhatia, Manjit K. Mohi, Anju Gupta, Shalini Singh

Abstract


Aggressive angiomyxoma a soft tissue tumor arising in the pelvis and perineal regions of women in reproductive age group is a rare entity. It is slow growing locally aggressive myxoid mesenchymal tumor, with a marked tendency to local recurrence. Preoperative clinical diagnosis is usually difficult due to absence of diagnostic features as well as rarity of the disease. We describe a case of aggressive angiomyxoma of vagina in a 47-year-old para 4 woman with multiple fibromyoma (upto 22-week size of pregnant uterus) with 10*10 cms posterior vaginal cyst. Total abdominal hystrectomy with surgical excision of vaginal wall cyst done. A retrospective diagnosis-Aggressive Angiomyxoma of the vagina was made after histological confirmation. Surgical excision with wide margins and long term follow up remains treatment of choice.


Keywords


Aggressive angiomyxoma, Retrospective diagnosis, Surgical excision

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References


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