DOI: http://dx.doi.org/10.18203/2320-1770.ijrcog20184547

Acardia anceps: the monster twin; twin reversed arterial perfusion (TRAP) syndrome

Shazia Khan, Tina Singh, Gunadhar Maiti

Abstract


Twin reversed arterial perfusion (TRAP) sequence is an extremely rare complication of monochorionic multi-foetal pregnancy, occurring once in 35,000 births. It is characterized by a malformed foetus without a heart being perfused by a structurally normal (pump) twin via an artery-to-artery anastomosis in a reverse direction. We report one such case where ultrasound imaging revealed monochorionic twin pregnancy with a viable, normal-appearing first twin and a structurally aberrant second twin with absent cardiac activity. The patient was monitored with two weekly ultrasonography and Doppler ultrasound examination to ascertain the well-being of the pump twin. She delivered successfully at term a normal live baby and an acardius anceps foetus. The perinatal mortality of the pump twin ranges from 35 to 55%; making it essential to diagnose the presence of a pump twin at an early gestational age through improved imaging techniques to plan effective intervention at appropriate time.


Keywords


Acardia anceps, Acardia twin, Monochorionic twin, TRAP sequence

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