Embryonal rhabdomyosarcoma of the uterine cervix: a rare case report
DOI:
https://doi.org/10.18203/2320-1770.ijrcog20164683Keywords:
Adolescent neoplasm, Embryonal rhabdomyosarcoma, Sarcoma botryoides, Uterine cervix neoplasmAbstract
Embryonal rhabdomyosarcoma of the female genital tract is a rare tumour. It tends to occur during childhood in the vagina and, rarely, it can arise in the uterine cervix, with a peak incidence in the second decade. We report a case of a 18-year-old female with an embryonal rhabdomyosarcoma (sarcoma botryoides) presenting himself as a cervical polyp. This tumour consisted of rhabdomyoblasts with miscellaneous differentiation surrounded by a loose, myxoid stroma. The patient was successfully treated with cervical conization and adjuvant chemotherapy. She is now disease-free at the 28th month follow-up. Awareness of this uncommon lesion in the cervix and its clinical implications is important to prevent misdiagnosis. Therapy has recently inclined to conservative and fertility-sparing treatment.
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