DOI: http://dx.doi.org/10.18203/2320-1770.ijrcog20194913

A rare case of conjoined twins presenting as dicephalus parapagus: a case report

Lakshmi Subburaj, Rajkumar K.

Abstract


Conjoined twinning is a congenital abnormality resulting in various presentations of the fetuses in utero. It is a rare embryological developmental disorder occurring in one in 100,000 births. We present a case of conjoined twinning, which is characterized by the presence of two heads, single vertebral column and single symphysis pubis, with single genitor-urinary tract and single gastro intestinal tract. The present condition, referred to as dicephalus parapagus, is a rare entity among the conjoined twinning and has seldom positive outcomes. The mechanism of occurrence of conjoined twinning has been proposed either through fusion or fission of the embryos. In either case, surgical separation of the conjoined twins is often unsuccessful and results in increased morbidity and mortality. However, it is essential to screen for the presence of such congenital anomalies early during pregnancy, in order to terminate and provide parental counselling.


Keywords


Anomaly scan, Conjoined twinning, Dicephalus parapagus, Embryology, High-risk pregnancy, Ultrasound

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References


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