Fibroid arising in a mullerian duct remnant presenting as a pelvic mass-sonographic diagnosis with magnetic resonance imaging correlation

Amandeep Singh, Gauravdeep Singh


Mullerian agenesis is a rare congenital anomaly characterized as aplasia or hypoplasia of uterus in women with normal development of secondary sex characteristics. Presence of leiomyoma in mullerian agenesis is very rare and only few cases have been reported in the literature.  Ultrasound and MRI showed a large soft tissue mass in right adnexal region. A provisional diagnosis of mullerian agenesis associated with two pelvic masses was made. Histopathology confirmed the diagnosis of leiomyoma.


Mullerian agenesis, Fibroid, Primary amenorrhoea

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