Ectopia cordis about a case at Ourossogui regional hospital center

Abdoulaye Diakhate; Mame D. N. Guèye; Abdou K. Diallo; Mouhamadou Wade; Simon B. Ndour; Daba Diop; Cheikh Dieng; Ameth Mbodji; Mamour Guèye

doi:10.18203/2320-1770.ijrcog20210348

Authors

Abdoulaye Diakhate Gynecological and Obstetrical Clinic of The Aristide Le Dantec University Hospital Center, Dakar, Senegal Maternity of Ourossogui Regional Hospital Center, Dakar, Senegal
Mame D. N. Guèye Gynecological and Obstetrical Clinic of The Aristide Le Dantec University Hospital Center, Dakar, Senegal
Abdou K. Diallo Gynecological and Obstetrical Clinic of The Aristide Le Dantec University Hospital Center, Dakar, Senegal
Mouhamadou Wade Gynecological and Obstetrical Clinic of The Aristide Le Dantec University Hospital Center, Dakar, Senegal
Simon B. Ndour Gynecological and Obstetrical Clinic of The Aristide Le Dantec University Hospital Center, Dakar, Senegal
Daba Diop Gynecological and Obstetrical Clinic of The Aristide Le Dantec University Hospital Center, Dakar, Senegal
Cheikh Dieng Maternity of Ourossogui Regional Hospital Center, Dakar, Senegal
Ameth Mbodji Maternity of Ourossogui Regional Hospital Center, Dakar, Senegal
Mamour Guèye Gynecological and Obstetrical Clinic of The Aristide Le Dantec University Hospital Center, Dakar, Senegal

DOI:

https://doi.org/10.18203/2320-1770.ijrcog20210348

Keywords:

Ectopia cordis, Cantrell syndrome, Extrathoracic heart

Abstract

We report in this work, an extremely rare and major case of anterior body wall defects included ectopia cordis define by abnormal location of heart outside of the thorax. This case was diagnosed at the maternity of Ourossogui regional hospital center, in Senegal. Any scan was performed during the pregnancy. Newborn died 10 minutes after birth. Ectopia cordis is related to a possible ventral midline developmental abnormality. It’s associated to other midline abnormalities and is a part of pentalogy of Cantrell. An X-linked genetic abnormality.

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