Complete pentalogy of Cantrell associated with exencephaly: a rare case report
Keywords:
Pentalogy of Cantrell, Ectopia cordis, Exencephaly, Abdominal wall defect, PCAbstract
Complete pentalogy of Cantrell (PC) is a rare condition with an incidence of 1 in 100000 pregnancies. The spectrum includes defects in the diaphragm, anterior abdominal wall, diaphragmatic pericardium, lower sternum and congenital cardiac anomalies. We hereby report a case of complete pentalogy of Cantrell associated with exencephaly.
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References
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